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Набута генералізована ліподистрофія

ORPHA:79086· ICD-10 E88.1· Acquired generalized lipodystrophy

Визначення(English summary)

A rare lipodystrophic syndrome characterized by loss of adipose tissue, and is a syndrome of insulin resistance that leads to increased cardiovascular risk. Acquired generalized lipodystrophy is related to a selective loss of subcutaneous adipose tissue occurring exclusively at the extremities (face, legs, arms, palms and sometimes soles).

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
All ages