Набута генералізована ліподистрофія
ORPHA:79086· ICD-10 E88.1· Acquired generalized lipodystrophy
Визначення(English summary)
A rare lipodystrophic syndrome characterized by loss of adipose tissue, and is a syndrome of insulin resistance that leads to increased cardiovascular risk. Acquired generalized lipodystrophy is related to a selective loss of subcutaneous adipose tissue occurring exclusively at the extremities (face, legs, arms, palms and sometimes soles).
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- All ages