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Порокератоз долонний та підошовний дисемінований

ORPHA:737· ICD-10 Q82.8· Porokeratosis plantaris palmaris et disseminata

Визначення(English summary)

A rare genetic disease which is a rare form of porokeratosis occurring mainly in adolescence and characterized by small pruritic or painful keratotic papules that first appear on the palms and soles, and may gradually spread to other body zones.

Поширеність
Unknown
Успадкування
Autosomal dominant, X-linked dominant
Вік початку
Adolescent, Adult