vitalwiki

Нирковий синдром Лускунчика

ORPHA:71273· ICD-10 Q27.8· Renal nutcracker syndrome

Визначення(English summary)

A rare, syndromic renal disease characterized by the entrapment of left renal vein (LRV) between the superior mesenteric artery (SMA) and the abdominal aorta, resulting in increased luminal pressure, renal hilar varices, hematuria and, at the microscopic level, rupture of thin-walled veins into the collecting system in renal fornices.

Поширеність
Unknown
Успадкування
Unknown
Вік початку
Adult