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Іридокорнеальний ендотеліальний синдром

ORPHA:64734· ICD-10 H21.1· Iridocorneal endothelial syndrome

Визначення(English summary)

Iridocorneal endothelial (ICE) syndrome describes a group of progressive corneal proliferative endotheliopathies comprised of Chandler’s syndrome, Cogan-Reese syndrome and essential iris atrophy (see these terms), affecting mainly young adult females and characterized by iris holes and atrophy, papillary distortion, anterior synechiae, corneal edema and often with secondary glaucoma and corneal decompensation as complications

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Adult