Несакральний обмежений дорсальний мієлошизис
ORPHA:645343· ICD-10 Q76.0· Non-saccular limited dorsal myeloschisis
Визначення(English summary)
A rare form of limited dorsal myeloschisis (LDM), characterized by a non saccular cutaneous stigmata (midline skin abnormality classically dimple, pit or sometimes angioma), the stalk is attached to this cutaneous stigmata. Fibroneural stalk varies in thickness and complexity.