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Фіброневрологічний несакральний обмежений дорсальний мієлошизис

ORPHA:645310· Fibroneural non-saccular limited dorsal myeloschisis

Визначення(English summary)

A rare non-saccular limited dorsal myeloschisis, in which the stalk histology is characterized by skin tissue with dermo-epidermal epithelium in continuity with a subcutaneous fibrocollagenous tract containing various ectopic tissues.