Фіброневрологічний несакральний обмежений дорсальний мієлошизис
ORPHA:645310· Fibroneural non-saccular limited dorsal myeloschisis
Визначення(English summary)
A rare non-saccular limited dorsal myeloschisis, in which the stalk histology is characterized by skin tissue with dermo-epidermal epithelium in continuity with a subcutaneous fibrocollagenous tract containing various ectopic tissues.