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Синдром PASS

ORPHA:641385· ICD-10 L88· PASS syndrome

Визначення(English summary)

A rare autoinflammatory syndrome characterized by a chronic-relapsing course of the combination of pyoderma gangrenosum, acne, hidradenitis suppurativa (which, in addition to axillae and inguinal folds, can be observed on upper and lower limbs, back, and buttocks, among others), and ankylosing spondylitis. Typical age of onset is adolescence to young adulthood, with the different signs and symptoms appearing simultaneously or subsequently.

Поширеність
<1 / 1 000 000
Вік початку
Adult