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Набута хвороба Крейтцфельдта-Якоба

ORPHA:454700· Acquired Creutzfeldt-Jakob disease

Визначення(English summary)

A group of human prion diseases characterized by progressive, invariably fatal neurodegeneration resulting from accidental transmission of prions. The group comprises iatrogenic Creutzfeldt-Jakob disease (CJD), which results from transmission of CJD prions in the course of medical procedures or treatments, and variant CJD (transmission via consumption of products from prion-diseased cows or via blood transfusion from an affected individual).

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
All ages