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Системний вузликовий поліартеріїт

ORPHA:439762· ICD-10 M30.0· Systemic polyarteritis nodosa

Визначення(English summary)

Systemic polyarteritis nodosa (PAN; see this term) is a chronic systemic necrotizingvasculitis of adults and childrenaffecting small- and medium-sized vessels and characterized by formation of microaneurysms leading to serious generalized disease and multi-organ involvement.

Успадкування
Not applicable