Системний вузликовий поліартеріїт
ORPHA:439762· ICD-10 M30.0· Systemic polyarteritis nodosa
Визначення(English summary)
Systemic polyarteritis nodosa (PAN; see this term) is a chronic systemic necrotizingvasculitis of adults and childrenaffecting small- and medium-sized vessels and characterized by formation of microaneurysms leading to serious generalized disease and multi-organ involvement.
- Успадкування
- Not applicable