Солідна псевдопапілярна карцинома підшлункової залози
ORPHA:424065· ICD-10 C25.1· Pancreatic solid pseudopapillary neoplasm
Визначення(English summary)
A rare carcinoma of the pancreas characterized by a variable combination of nonspecific signs and symptoms, such as abdominal pain, jaundice, abdominal fullness, anorexia, nausea, vomiting, and weight loss. One-third of the patients are asymptomatic. The tumor has low malignant potential, but can invade locally.
- Поширеність
- <1 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- Adult