vitalwiki

Хондроміксоїдна фіброма

ORPHA:404507· ICD-10 D16.9· Chondromyxoid fibroma

Визначення(English summary)

A rare bone tumor characterized by a benign lesion composed of lobules of spindle shaped or stellate cells and an abundant myxoid or chondroid matrix. The tumor may occur in almost any osseous location but is most common in long bones, in particular the proximal tibia and the distal femur. Pain is the most common presenting symptom. Prognosis is excellent even in cases with local recurrence.

Поширеність
<1 / 1 000 000
Успадкування
Not applicable
Вік початку
Adolescent, Adult, Childhood, Elderly