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ORPHA:3465· ICD-10 G80.8· Worster-Drought syndrome

Визначення(English summary)

Worster-Drought syndrome (WDS) is a form of cerebral palsy characterized by congenital pseudobulbar (suprabulbar) paresis manifesting as selective weakness of the lips, tongue and soft palate, dysphagia, dysphonia, drooling and jaw jerking.

Поширеність
1-9 / 100 000
Успадкування
Autosomal dominant, Not applicable
Вік початку
Childhood