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Актинічне пруріго

ORPHA:330061· ICD-10 L56.4· Actinic prurigo

Визначення(English summary)

A rare, chronic, photodermatosis disease characterized by intensely pruritic, polymorphic, erythematous, excoriated and/or lichenified papules, macules, plaques and nodules, occurring on sun-exposed areas of the skin (particularly face, nose, lips, and ears), frequently associating cheilitis (especially of the lower lip) and conjuctivitis, which are present year-round or only in the spring/summer (depending on geographic location), observed mainly in Native Americans and Mestizos. Cheilitis may be the sole clinical presentation. Histologically, the presence of lymphoid follicles in mucosa is pathognomonic.

Поширеність
Unknown
Успадкування
Multigenic/multifactorial, Not applicable
Вік початку
Childhood