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Кальцифілаксія шкіри

ORPHA:280065· ICD-10 E83.5· Calciphylaxis cutis

Визначення(English summary)

A rare, life-threatening, non-inflammatory vasculopathy characterized clinically by progressive and painful skin lesions associated with calcification of cutaneous arterial microvessels. Calciphylaxis predominantly affects patients with end-stage kidney disease (ESKD) on dialysis.