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Множинні ендокринні неоплазії, тип 4

ORPHA:276152· ICD-10 D44.8· Multiple endocrine neoplasia type 4

Визначення(English summary)

Multiple endocrine neoplasia type 4 (MEN4) is a very rare form of MEN (see this term), an inherited cancer syndrome, characterized by parathyroid and anterior pituitary tumors, possibly associated with adrenal, renal, and reproductive organ tumors.

Поширеність
Unknown
Успадкування
Autosomal dominant, Not applicable
Вік початку
Adult