Множинні ендокринні неоплазії, тип 4
ORPHA:276152· ICD-10 D44.8· Multiple endocrine neoplasia type 4
Визначення(English summary)
Multiple endocrine neoplasia type 4 (MEN4) is a very rare form of MEN (see this term), an inherited cancer syndrome, characterized by parathyroid and anterior pituitary tumors, possibly associated with adrenal, renal, and reproductive organ tumors.
- Поширеність
- Unknown
- Успадкування
- Autosomal dominant, Not applicable
- Вік початку
- Adult