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Анапластична/великоклітинна медулобластома

ORPHA:251855· ICD-10 C71.6· Anaplastic/large cell medulloblastoma

Визначення(English summary)

A histological variant of medulloblastoma, an embryonic malignancy, associated with extremely low survival rates and a high risk of metastatic disease and manifesting with symptoms of increased intracranial pressure such as vomiting, headache, listlessness, papilledema and diplopia.

Вік початку
Infancy, Neonatal