vitalwiki

Ліпобластома

ORPHA:247762· ICD-10 D17.9· Lipoblastoma

Визначення(English summary)

A rare soft tissue tumor characterized by a lobulated, localized (lipoblastoma) or diffuse (lipoblastomatosis) lesion resembling fetal adipose tissue, composed of mature and immature adipocytes. It is most commonly found during the first years of life and presents as a slowly growing, well circumscribed mass, which may compress adjacent structures, depending on the location. Malignant transformation or metastasis does not occur, while recurrences are described especially in lipoblastomatosis.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Childhood