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Генералізований пустульозний псоріаз

ORPHA:247353· ICD-10 L40.1· Generalized pustular psoriasis

Визначення(English summary)

Generalized pustular psoriasis is a severe inflammatory skin disease that can be life-threatening and that is characterized by recurrent episodes of high fever, fatigue, episodic erythematous cutaneous eruptions with sterile cutaneous pustules formation on various parts of the body, and neutrophil leukocytosis.

Поширеність
1-9 / 1 000 000
Успадкування
Autosomal recessive, Not applicable
Вік початку
Adult