Класичний синдром прогресуючого надядерного паралічу
ORPHA:240071· ICD-10 G23.1· Classic progressive supranuclear palsy syndrome
Визначення(English summary)
A classical form of progressive supranuclear palsy (PSP), a rare late-onset neurodegenerative disease, characterized by slowing of vertical saccadic eye movements, falls due to postural instability, axial akinetic-rigid syndrome, and cognitive impairment. Difficulties in speech and swallowing may develop.
- Поширеність
- 1-9 / 100 000
- Успадкування
- Not applicable
- Вік початку
- Adult