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Класичний синдром прогресуючого надядерного паралічу

ORPHA:240071· ICD-10 G23.1· Classic progressive supranuclear palsy syndrome

Визначення(English summary)

A classical form of progressive supranuclear palsy (PSP), a rare late-onset neurodegenerative disease, characterized by slowing of vertical saccadic eye movements, falls due to postural instability, axial akinetic-rigid syndrome, and cognitive impairment. Difficulties in speech and swallowing may develop.

Поширеність
1-9 / 100 000
Успадкування
Not applicable
Вік початку
Adult