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Хвороба Кавасакі

ORPHA:2331· ICD-10 M30.3· Kawasaki disease

Визначення(English summary)

A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated.

Поширеність
Unknown
Успадкування
Multigenic/multifactorial
Вік початку
Adolescent, Adult, Childhood, Infancy