Аутоімунна поліендокринопатія, тип 4
ORPHA:227990· ICD-10 E31.0· Autoimmune polyendocrinopathy type 4
Визначення(English summary)
A rare autoimmune polyendocrinopathy characterized by autoimmune activity against an endocrine organ in combination with at least one more endocrine or non-endocrine organ. Typical autoimmune diseases occurring in this type include insulin-requiring diabetes, pernicious anemia, alopecia, vitiligo, or myasthenia gravis, but not Addison disease, thyroid disease, or hypoparathyroidism.
- Успадкування
- Multigenic/multifactorial
- Вік початку
- Adult