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Аутоімунна поліендокринопатія, тип 4

ORPHA:227990· ICD-10 E31.0· Autoimmune polyendocrinopathy type 4

Визначення(English summary)

A rare autoimmune polyendocrinopathy characterized by autoimmune activity against an endocrine organ in combination with at least one more endocrine or non-endocrine organ. Typical autoimmune diseases occurring in this type include insulin-requiring diabetes, pernicious anemia, alopecia, vitiligo, or myasthenia gravis, but not Addison disease, thyroid disease, or hypoparathyroidism.

Успадкування
Multigenic/multifactorial
Вік початку
Adult