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Фокальна долонно-підошовна та ясенна кератодермія

ORPHA:2200· ICD-10 Q82.8· Focal palmoplantar and gingival keratoderma

Визначення(English summary)

Focal palmoplantar and gingival keratoderma is a very rare form of focal palmoplantar keratoderma characterized by painful circumscribed hyperkeratotic lesions on weight-bearing areas of soles, moderate focal hyperkeratosis of palmar pressure-related areas and an asymptomatic leukokeratosis confined to labial- and lingual- attached gingiva. Additional occasional features may include hyperhidrosis, follicular keratosis and extended oral mucosa involvement.

Поширеність
<1 / 1 000 000
Вік початку
Childhood