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Гліома зорового тракту

ORPHA:2086· ICD-10 D33.3· Optic pathway glioma

Визначення(English summary)

Optic pathway glioma (OPG) is a benign tumor that develop along the optic nerve (chiasm, tracts, and radiations) characterized by impairment or loss of vision and may be accompanied by diencephalic symptoms such as reduced growth and alteration in sleeping patterns. OPG are often linked to neurofibromatosis type 1 (NF1, see this term).

Поширеність
1-9 / 1 000 000
Успадкування
Not applicable
Вік початку
All ages