Атрезія хоан, двостороння
ORPHA:137920· ICD-10 Q30.0· Choanal atresia, bilateral
Визначення(English summary)
A rare, usually sporadic, congenital nose and cavum anomaly characterized by respiratory distress relieved by crying and rhinorrhea that presents at birth. It is caused by blockade of the nose on both sides by bony or soft tissue formed during embryological development.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- Infancy, Neonatal