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Атрезія хоан, двостороння

ORPHA:137920· ICD-10 Q30.0· Choanal atresia, bilateral

Визначення(English summary)

A rare, usually sporadic, congenital nose and cavum anomaly characterized by respiratory distress relieved by crying and rhinorrhea that presents at birth. It is caused by blockade of the nose on both sides by bony or soft tissue formed during embryological development.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Infancy, Neonatal