Первинний шкірний амілоїдоз
ORPHA:137807· Primary cutaneous amyloidosis
Визначення(English summary)
A rare group of skin diseases characterized histologically by the extracellular accumulation of amyloid deposits in the dermis. Rare forms include lichen amyloidosus, X-linked reticulate pigmentary disorder, primary localized cutaneous nodular amyloidosis, and macular amyloidosis.
- Поширеність
- Unknown
- Успадкування
- Autosomal dominant, Not applicable
- Вік початку
- All ages