Прогресуюча геміфаціальна атрофія
ORPHA:1214· ICD-10 G51.8· Progressive hemifacial atrophy
Визначення(English summary)
Progressive hemifacial atrophy (PHA) is a rare acquired disorder, characterized by unilateral slowly progressive atrophy of the skin and soft tissues of half of the face leading to a sunken appearance. Muscles, cartilage and the underlying bony structures may also be involved.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- Adolescent, Adult, Childhood