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Атрезія уретри

ORPHA:105· ICD-10 Q64.3· Atresia of urethra

Визначення(English summary)

A rare fetal lower urinary tract obstruction (LUTO) characterized by closure or failure to develop an opening in the urethra and resulting in obstructive uropathy presenting in utero as megacystis, oligohydramnios or anhydramnios, and potter sequence.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Antenatal, Neonatal