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Genetic recurrent myoglobinuria

ORPHA:99845· ICD-10 R82.1

Definition

Genetic recurrent myoglobinuria is an inborn error of metabolism characterized by abnormal urinary excretion of myoglobin due to acute destruction of skeletal muscle fibers.

Prevalence
Unknown
Inheritance
Autosomal dominant, Autosomal recessive, Not applicable
Age of onset
Childhood