Unilateral multicystic dysplastic kidney
ORPHA:97363· ICD-10 Q61.4
Definition
A rare form of multicystic dysplastic kidney (MCDK), a congenital anomaly of the kidney and urinary tract (CAKUT), in which one kidney is large, distended by multiple cysts, and non-functional.
- Prevalence
- 1-5 / 10 000
- Inheritance
- Autosomal dominant
- Age of onset
- All ages