Amyotrophic lateral sclerosis
ORPHA:803· ICD-10 G12.2
Definition
A neurodegenerative disease characterized by progressive muscular paralysis reflecting degeneration of motor neurons in the primary motor cortex, corticospinal tracts, brainstem and spinal cord.
- Prevalence
- 1-9 / 100 000
- Inheritance
- Autosomal dominant, Autosomal recessive, Not applicable
- Age of onset
- Adult