Idiopathic acute eosinophilic pneumonia
ORPHA:724· ICD-10 J82
Definition
Idiopathic acute eosinophilic pneumonia (IAEP) is an eosinophilic pneumonia of undetermined etiology that is characterized by acute febrile hypoxic respiratory failure associated with diffuse radiographic infiltrates and pulmonary eosinophilia, but without concurring allergy or infection.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Unknown
- Age of onset
- All ages