Rhabdoid tumor
ORPHA:69077· ICD-10 C49.9
Definition
Rhabdoid tumor (RT) is an aggressive pediatric soft tissue sarcoma that arises in the kidney, the liver, the peripheral nerves and all miscellaneous soft-parts throughout the body. RT involving the central nervous system (CNS) is called atypical teratoid rhabdoid tumor (ATRT).
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- Antenatal, Childhood, Infancy, Neonatal