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Non-syndromic bilambdoid craniosynostosis

ORPHA:620178· ICD-10 Q75.0

Definition

A form of non-syndromic multisutural craniosynostosis characterized by bilateral premature fusion of the lambdoid sutures, resulting in flattening and widening of the entire occipital region, with compensatory bossing of the vertex region (giving the cranium an elongated shape), and anterior-posterior displacement of the ears.

Prevalence
<1 / 1 000 000
Age of onset
Neonatal