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Non-syndromic unicoronal craniosynostosis

ORPHA:620102· ICD-10 Q75.0

Definition

A form of non-syndromic unisutural craniosynostosis characterized by the premature fusion of one of the two coronal sutures of the newborn, leading to plagiocephaly with flattening of the ipsilateral side of the forehead and a compensatory bulging of the contralateral side. Ocular anomalies (strabismus, hypermetropia, astigmatism) due to orbital dystopia, and ocular torticollis, are commonly associated with in unicoronal craniosynostosis.

Prevalence
1-9 / 1 000 000
Age of onset
Neonatal