Caroli disease
ORPHA:53035· ICD-10 Q44.6
Definition
Caroli disease (CD) is a rare congenital liver disease characterized by non-obstructive cystic dilatations of the intra-hepatic and rarely extra-hepatic bile ducts.
- Prevalence
- 1-9 / 1 000 000
- Inheritance
- Autosomal recessive, Not applicable
- Age of onset
- All ages