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Carcinoma of esophagus, salivary gland type

ORPHA:418945· ICD-10 C15.1

Definition

A rare gastroesophageal tumor characterized by a typically submucosal tumor occurring usually in the middle to distal esophagus and histologically characterized as either mucoepidermoid (intimate mixture of mucus, intermediate, and epidermoid cells) or as adenoid cystic carcinoma (biphasic admixture of duct‐lining epithelial and myoepithelial cells with tubular, cribriform, solid, or basaloid growth patterns). Patients may be asymptomatic or may present with progressive dysphagia, heartburn, retrosternal pain and/or weight loss.

Prevalence
<1 / 1 000 000
Inheritance
Not applicable
Age of onset
Adult, Elderly