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Gyrate atrophy of choroid and retina

ORPHA:414· ICD-10 E72.4

Definition

Gyrate atrophy of the choroid and retina (GACR) is a very rare, inherited retinal dystrophy, characterized by progressive chorioretinal atrophy, myopia and early cataract.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Childhood