Neonatal scleroderma
ORPHA:398127· ICD-10 P83.8
Definition
A rare secondary neonatal autoimmune disease characterized by neonatal-onset of erythematous skin lesions with a linear appearance that gradually become indurated and hyperpigmented and progressively present skin atrophy. Positive serum antibodies (in particular antinuclear antibodies and/or rheumatoid factor) may be associated.
- Prevalence
- <1 / 1 000 000
- Age of onset
- Neonatal