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Wild type ATTR amyloidosis

ORPHA:330001· ICD-10 E85.8

Definition

A common form of systemic amyloidosis characterized by deposition of wild type transthyretin predominantly in the heart and the soft tissues (mainly the carpal tunnel region, lumbar canal and tendons).

Prevalence
1-5 / 10 000
Inheritance
Not applicable
Age of onset
Adult, Elderly