Monoamine oxidase A deficiency
ORPHA:3057· ICD-10 E70.8
Definition
Monoamine oxidase-A deficiency is a very rare recessive X-linked biogenic amine metabolism disorder characterized clinically by mild intellectual deficit, impulsive aggressiveness, and sometimes violent behavior and presenting from childhood.
- Prevalence
- Unknown
- Inheritance
- X-linked recessive
- Age of onset
- Childhood