vitalwiki

Infantile myofibromatosis

ORPHA:2591· ICD-10 D48.1

Definition

A rare benign soft tissue tumor characterized by the development of nodules in the skin, striated muscles, bones, and in exceptional cases, visceral organs, leading to a broad spectrum of clinical symptoms. It contains myofibroblasts.

Prevalence
Unknown
Inheritance
Autosomal dominant, Autosomal recessive, Not applicable
Age of onset
Antenatal, Infancy, Neonatal