vitalwiki

Mayer-Rokitansky-Küster-Hauser syndrome type 1

ORPHA:247775· ICD-10 Q51.8

Definition

Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome type 1, a form of MRKH syndrome, is an isolated form of congenital aplasia of the uterus and 2/3 of the vagina occurring in otherwise phenotypically normal females.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant, Not applicable
Age of onset
Adolescent, Antenatal