Systemic mastocytosis
ORPHA:2467· ICD-10 C96.2
Definition
A heterogeneous group of rare, acquired and chronic hematological malignancies related to an abnormal accumulation/proliferation of neoplastic mast cells (MCs) in one or several organs, mainly the bone marrow (BM), associated frequently with skin involvement.
- Prevalence
- 1-5 / 10 000
- Inheritance
- Not applicable
- Age of onset
- All ages