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Léri-Weill dyschondrosteosis

ORPHA:240· ICD-10 Q77.8

Definition

A rare, genetic skeletal dysplasia marked by disproportionate short stature and the characteristic Madelung wrist deformity.

Prevalence
Unknown
Inheritance
Autosomal dominant
Age of onset
Adolescent, Antenatal, Childhood, Infancy, Neonatal