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Episodic ataxia type 7

ORPHA:209970· ICD-10 G11.8

Definition

Episodic ataxia type 7 (EA7) is an exceedingly rare form of Hereditary episodic ataxia characterized by ataxia with weakness, vertigo, and dysarthria without interictal findings.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Childhood