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Multinodular goiter-cystic kidney-polydactyly syndrome

ORPHA:2091· ICD-10 Q87.8

Definition

Multinodular goiter - cystic kidney - polydactyly syndrome is a very rare syndrome characterized by the association of multinodular goiter, cystic renal disease and digital anomalies.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Antenatal, Neonatal