Idiopathic pulmonary fibrosis
ORPHA:2032· ICD-10 J84.1
Definition
An interstitial lung disease with a poor prognosis, that is characterized by the progressive formation of scar tissue within the lungs in the absence of any known cause.
- Prevalence
- 1-5 / 10 000
- Inheritance
- Multigenic/multifactorial
- Age of onset
- Adult