Brugada syndrome
ORPHA:130· ICD-10 I49.8
Definition
A cardiac disorder characterized on electrocardiogram (ECG) by ST segment elevation with a coved aspect on the right precordial leads, and a clinical susceptibility to ventricular tachyarrhythmias and sudden death occurring in the absence of overt myocardial abnormalities.
- Prevalence
- 1-5 / 10 000
- Inheritance
- Autosomal dominant, Not applicable
- Age of onset
- Adult, Childhood