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Arthrogryposis-like hand anomaly-sensorineural deafness syndrome

ORPHA:1144· ICD-10 Q68.8

Definition

A rare syndrome characterized by an arthrogryposis-like hand anomaly and sensorineural deafness. It has been described in only one family. Male-to-male transmission was observed.

Prevalence
<1 / 1 000 000
Inheritance
Unknown
Age of onset
Neonatal