Malignant Sertoli-Leydig cell tumor of the ovary
ORPHA:99916· ICD-10 C56
Definition
A rare malignant sex cord stromal tumor of ovary occuring typically in young women and characterized by manifestations of androgen excess (hirsutism, hair loss, amenorrhea, or oligomenorrhea), when functional.
- Prevalence
- <1 / 1 000 000
- Age of onset
- Adolescent, Adult, Childhood, Elderly